Myomas in uterine rudiments in a patient with Mayer-Rokitansky-Küster-Hauser syndrome

Authors: Hricko M. 1;  Chmel R. jr. 1,2;  Pastor Z. 1
Authors‘ workplace: Gynekologicko-porodniká klinika, 2. LF UK a FN Motol, Praha 2 LF UK v Plzni 1
Published in: Ceska Gynekol 2021; 86(1): 36-39
Category: Case Report
doi: 10.48095/cccg202136


Objective: To describe the case of a patient with Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome and a history of chronic pelvic pain due to myomas in the rudimentary uterine horns. The article highlights a rare origin of gynaecological pain.

Case report: We present the case of 61-year-old woman with MRKH syndrome who has suffered from chronic abdominal pain for more than one year before surgery. Using magnetic resonance imaging and ultrasonography, a suspicion on the tumours of uterine myoma character in the rudimentary horns was suggested. It was confirmed by laparoscopy. Myomas were removed in the endobag and histopathologically confirmed.

Conclusion: MRKH syndrome is a very rare disease. Approximately ten women are annually born with this congenital anomaly in the Czech Republic. While myoma incidence is extremely rare in this group of women, it must be taken into account in differential dia­gnosis and solved surgically in time.


Mayer-Rokitansky-Küster-Hauser syndrome – rudimentary uterine horn – myoma uteri


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Paediatric gynaecology Gynaecology and obstetrics Reproduction medicine

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